bims-hemali Biomed News
on Hematologic malignancies
Issue of 2026–09–27
twenty-two papers selected by
Alexandros Alexandropoulos, Γενικό Νοσοκομείο Αθηνών Λαϊκό



  1. Blood. 2026 Sep 24. 148(13): 1642-1644
      
    DOI:  https://doi.org/10.1182/blood.2026034920
  2. Blood. 2026 Sep 25. pii: blood.2026035238. [Epub ahead of print]
      In relapsed or refractory (R/R) B-cell acute lymphoblastic leukemia (ALL) and lymphoblastic lymphoma (LBL), responses to the CD22 antibody-drug conjugate inotuzumab ozogamicin (INO) are frequent but short-lived. Based on preclinical evidence of synergy, we conducted a phase 1 trial of the BCL-2 inhibitor venetoclax (VEN) plus standard-dose INO for adults with R/R CD22+ ALL/LBL. Twenty-three patients enrolled (15 ALL, 8 LBL): three at dose level 1 (DL1; VEN 200 mg/day), six at DL2 (VEN 400 mg/day), and fourteen in an expansion cohort (VEN 400 mg/day). The recommended dose was VEN 400 mg/day for 21 days per cycle. No dose-limiting toxicities or early mortality occurred. Patients received a median of 2 cycles (range 1-5). The most common grade ³3 adverse events were thrombocytopenia (43.5%) and neutropenia (39.1%). Four patients (17.4%) developed sinusoidal obstructive syndrome. Of 22 evaluable patients, 21 (95.5%) achieved complete remission, including 19 after one cycle. Measurable residual disease (MRD) cleared in 16/18 (88.9%) by flow cytometry (<10-4) and 14/19 (73.7%) by next-generation sequencing (<10-6). Fourteen (63.6%) patients proceeded to HSCT. With a median follow-up of 25.3 months (95% CI 19.0-32.4), two-year disease-free (DFS) and overall survival (OS) were 48% (95% CI 24-72%); median DFS was 22.1 months (95% CI 10.4-NA), and median OS was not reached. MRD-positivity was associated with lower baseline BCL-2 dependence. Correlates of progression included acquired MCL-1 dependence, CD22 antigen escape, drug efflux gene ABCB1 expression, and oncogenic mutations. In summary, VEN+INO is safe and effective for R/R B-ALL/LBL, producing frequent and durable MRD-negative remissions. NCT05016947.
    DOI:  https://doi.org/10.1182/blood.2026035238
  3. J Clin Oncol. 2026 Sep 25. JCO2600401
      The phase III CEPHEUS trial (ClinicalTrials.gov identifier: NCT03652064) of patients with transplant-ineligible (TIE) or transplant-deferred newly diagnosed multiple myeloma (NDMM; N = 395) demonstrated improved overall minimal residual disease (MRD) negativity rates among patients achieving ≥complete response and progression-free survival (PFS) with daratumumab plus bortezomib, lenalidomide, and dexamethasone (DVRd) versus VRd. We present efficacy and safety outcomes in the CEPHEUS TIE subgroup (N = 289; DVRd, n = 144; VRd, n = 145). Patients were either age 18-70 years with ≥1 comorbidity likely to negatively affect tolerability of high-dose chemotherapy with autologous stem cell transplantation or age ≥70 years. At a median follow-up of 58.7 months, the MRD negativity rate (10-5) was 60.4% (DVRd) versus 39.3% (VRd; P = .0004). Rates of sustained MRD negativity (10-5) for ≥12 months (47.2% v 28.3%; P = .0010) and ≥24 months (40.3% v 22.8%; P = .0015) were significantly higher with DVRd. Risk of disease progression or death was 49% lower for DVRd versus VRd (hazard ratio [HR], 0.51 [95% CI, 0.35 to 0.74]; P = .0003). Although immature, overall survival favored DVRd (HR, 0.66 [95% CI, 0.42 to 1.03]). Adverse events were consistent with known safety profiles. This analysis demonstrates that the deep responses achieved with DVRd translate into improved PFS in patients with TIE NDMM, reinforcing DVRd as a standard of care.
    DOI:  https://doi.org/10.1200/JCO-26-00401
  4. Leuk Res. 2026 Sep 18. pii: S0145-2126(26)00168-2. [Epub ahead of print]170 108324
      
    Keywords:  CML; Familial disease
    DOI:  https://doi.org/10.1016/j.leukres.2026.108324
  5. Blood Adv. 2026 Sep 24. pii: bloodadvances.2026021352. [Epub ahead of print]
      Primary central nervous system lymphoma is an aggressive lymphoma for which high-dose chemotherapy followed by autologous stem cell transplantation is standard first-line treatment in eligible patients; however, the optimal induction regimen remains uncertain. We conducted a multicenter international retrospective study across 11 centers including 355 transplant-eligible patients treated with MATRix (n=164), R-MPV/R-MT (n=121), or the reduced-intensity Alberta protocol (n=70). The overall response rate was 89.5%, with a complete response rate of 50.1%. Although complete response rates were higher with R-MPV/R-MT, transplantation rates were similar across regimens (74.4%, 69.4%, and 78.6%, respectively; p=0.36). Two-year overall survival was 79.0%, 89.0%, and 82.1% (p=0.32), and 2-year progression-free survival was 63.7%, 72.6%, and 75.3% (p=0.26) for MATRix, R-MPV/R-MT, and Alberta, respectively. Comparable outcomes were also observed among patients proceeding to transplantation (n=261). Toxicity however differed substantially between regimens: MATRix was associated with higher rates of dose reductions (p=0.006), ICU admissions (p<0.001), and treatment-related mortality (p=0.006). After adjustment for baseline imbalances using inverse probability of treatment weighting, survival outcomes remained comparable across treatment groups, whereas MATRix retained a less favorable toxicity profile. Less intensive induction regimens achieved transplantation and survival outcomes comparable to MATRix while demonstrating superior tolerability, supporting treatment strategies that optimize tolerability without compromising long-term outcomes.
    DOI:  https://doi.org/10.1182/bloodadvances.2026021352
  6. Lancet Oncol. 2026 Sep 25. pii: S1470-2045(26)00450-X. [Epub ahead of print]
    EXCALIBER-RRMM Investigators
       BACKGROUND: Iberdomide, a cereblon E3 ligase modulator with enhanced antimyeloma and immunostimulatory activity compared with immunomodulatory drugs, has shown clinical activity in relapsed or refractory multiple myeloma and synergy with anti-CD38 antibodies. EXCALIBER-RRMM, comparing iberdomide, daratumumab, and dexamethasone with daratumumab, bortezomib, and dexamethasone, uses minimal residual disease (MRD)-negative complete response and progression-free survival as dual primary endpoints. Here, we report the results of the primary analysis of MRD-negative complete response.
    METHODS: EXCALIBER-RRMM is an ongoing, two-stage, open-label, randomised, controlled, phase 3 trial done at 211 hospital and community-based sites in 31 countries. Eligible participants were adults (aged ≥18 years) with relapsed or refractory multiple myeloma, who had undergone one to two previous lines of therapy, had an Eastern Cooperative Oncology Group performance-status score of 0-2, achieved at least a partial response to previous treatment, and subsequently experienced disease progression. Patients with anti-CD38-refractory disease or bortezomib-refractory disease were excluded from both stages, whereas stage 2 permitted enrolment of up to 10% of patients with previous anti-CD38 exposure. Patients were randomly assigned (1:1:1:1 in stage 1 and 1:1 in stage 2) using interactive response technology to iberdomide, daratumumab, and dexamethasone or daratumumab, bortezomib, and dexamethasone. In stage 1, patients received iberdomide, daratumumab, and dexamethasone (oral iberdomide [1·0 mg, 1·3 mg, or 1·6 mg]; subcutaneous daratumumab [1800 mg]; and oral dexamethasone [40 mg or 20 mg for patients older than 75 years]) or daratumumab, bortezomib, and dexamethasone (subcutaneous daratumumab [1800 mg]; subcutaneous bortezomib [1·3 mg/m2]; and oral dexamethasone [20 mg]). In stage 2, patients received iberdomide (1·0 mg), daratumumab, and dexamethasone or daratumumab, bortezomib, and dexamethasone, all at the same doses and schedules as in stage 1. Treatment was received until confirmed disease progression, unacceptable toxicity, discontinuation, or withdrawal of consent. Dual primary endpoints were MRD-negative complete response at any time and progression-free survival. MRD was assessed in patients with suspected complete response or better. The primary analysis of MRD-negative complete response, reported here, was performed once the first 420 patients (intention-to-treat [ITT] population) had at least 12 months of follow-up (or discontinued early). Progression-free survival assessment is ongoing in a larger confirmatory cohort of 800 patients. Safety was assessed in all participants who received at least one dose of study treatment. This study is registered with ClinicalTrials.gov, NCT04975997, and is ongoing (active, not recruiting).
    FINDINGS: 1163 patients were screened for eligibility of whom 939 patients were randomised, 279 in stage 1 and 660 in stage 2. 800 patients were randomised to the 1·0-mg dose of iberdomide, daratumumab, and dexamethasone or to daratumumab, bortezomib, and dexamethasone. The primary MRD analysis ITT population comprised the first 420 patients enrolled between July 14, 2022, and July 3, 2024: 207 in the iberdomide, daratumumab, and dexamethasone group and 213 in the daratumumab, bortezomib, and dexamethasone group. Of these 420 patients, 244 [58%] were male, 176 [42%] were female, median age was 68 years [IQR 60-73], and 257 [61%] were White. At a median follow-up of 15·7 months (IQR 12·8-23·2), MRD-negative complete response was achieved in 85 (41%) of 207 patients receiving iberdomide, daratumumab, and dexamethasone and 44 (21%) of 213 receiving daratumumab, bortezomib, and dexamethasone (stratified proportion difference 20·1% [95% CI 11·5-28·6, p<0·0001]; odds ratio 2·8 [95% CI 1·8-4·3]). Grade 3 or grade 4 adverse events occurred in 187 (92%) of 204 patients with iberdomide, daratumumab, and dexamethasone and 143 (70%) of 204 patients with daratumumab, bortezomib, and dexamethasone, including neutropenia (172 [84%] vs 23 [11%]) and infection (80 [39%] vs 44 [22%]). Serious adverse events occurred in 119 (58%) patients in the iberdomide, daratumumab, and dexamethasone group and in 83 (41%) patients in the daratumumab, bortezomib, and dexamethasone group; the most common was pneumonia (36 [18%] vs 13 [6%]). Three (1%) deaths (sepsis, listeria encephalitis, and unknown cause) in the iberdomide, daratumumab, and dexamethasone group and two (1%) deaths (one due to sepsis and pneumonia and one due to sepsis) in the daratumumab, bortezomib, and dexamethasone group were considered related to any study treatment by the investigator.
    INTERPRETATION: Iberdomide, daratumumab, and dexamethasone significantly improved MRD-negative complete response compared with daratumumab, bortezomib, and dexamethasone. The most common grade 3 or grade 4 adverse events were haematological events and infections, which were mostly manageable with standard supportive care. These findings support iberdomide, daratumumab, and dexamethasone as an efficacious treatment option for patients with relapsed or refractory multiple myeloma with the potential to be administered across diverse care settings. Assessment of progression-free survival, the second dual primary endpoint, is ongoing.
    FUNDING: Bristol Myers Squibb.
    DOI:  https://doi.org/10.1016/S1470-2045(26)00450-X
  7. Blood Adv. 2026 Sep 24. pii: bloodadvances.2026021214. [Epub ahead of print]
      Relapsed or refractory lymphoma carries poor prognosis, with limited options after standard therapies. Spleen tyrosine kinase (SYK) mediates B-cell receptor and aberrant T-cell receptor signaling, promoting survival and proliferation. HMPL-523 (sovleplenib) is a novel, selective oral SYK inhibitor with preclinical activity in lymphoid malignancies. This Phase 1, open-label, multicenter study (NCT03779113) enrolled adult patients with relapsed/refractory lymphoma who had exhausted approved therapies. The trial included dose escalation (100-800 mg once daily) and expansion (700 mg once daily) stages across multiple lymphoma subtypes. Safety was assessed per NCI CTCAE v5.0; efficacy per Lugano 2014 and disease-specific criteria. Sixty-nine patients were treated (Stage 1: n=21; Stage 2: n=48). The recommended Phase 2 dose was 700 mg once daily; the maximum tolerated dose was not reached. Common grade ≥3 treatment-emergent adverse events included neutropenia, elevated liver enzymes, and thrombocytopenia; no treatment-related deaths occurred. Among 53 response-evaluable patients across stage 1 and stage 2 who were treated at the recommended Phase 2 dose or above, overall response rate (ORR) was 30.2%, including 5 complete responses. ORR by key cohort was 25.9% for Hodgkin lymphoma (n=27), 28.6% for chronic lymphocytic leukemia post-Bruton's tyrosine kinase inhibitor (n=7), and 33.3% for peripheral T-cell lymphoma (n=9), with a median duration of response ranging from 5.7 to 11.3 months. Pharmacokinetic analysis showed dose-proportional exposure and ~2-fold accumulation with daily dosing. Sovleplenib demonstrated a safety profile managed with supportive medications, predictable pharmacokinetics, and preliminary antitumor activity in heavily pretreated lymphoma patients, supporting further investigation in combination and earlier-line settings. ClinicalTrials.gov Identifier: NCT03779113.
    DOI:  https://doi.org/10.1182/bloodadvances.2026021214
  8. Br J Haematol. 2026 Sep 22.
    Australasian Leukaemia and Lymphoma Group
      SeaLAND (ALLG MM23, ACTRN12620000291987) was a randomized, open-label phase III study evaluating low-dose weekly selinexor (40 mg) plus lenalidomide (selinexor-R) versus lenalidomide alone (R) as post-transplant maintenance therapy for newly diagnosed, transplant-eligible multiple myeloma. A total of 142 patients were enrolled (R = 64; selinexor-R = 78); the trial closed early for futility. At best response, the complete response (≥CR) rate was numerically, but not significantly, higher with selinexor-R than R (67% vs. 53%, p = 0.09). At 24 months median follow-up, progression-free survival (PFS) was not significantly different between selinexor-R compared to R (hazard ratio [HR] = 1.22; 95% confidence interval [CI] 0.62-2.41; p = 0.56); 24-month PFS rates were 73% (95% CI 57%-84%) for R and 70% (95% CI: 56%-81%) for selinexor-R. The mean relative dose intensity (RDI) of R was lower in the selinexor-R arm compared to R alone (68% vs. 81%, p = 0.002); the mean RDI of S was 55%. Grade ≥3 adverse events were more frequent with selinexor-R (85% vs. 45%, p < 0.001). Common severe non-haematological adverse events included infections (R: 6%, selinexor-R: 19%, p < 0.01) and gastrointestinal disorders (R: 3%, selinexor-R: 14%, p < 0.05). Selinexor-R maintenance did not improve PFS and substantially increased toxicity. Selinexor-R maintenance cannot be recommended for the general myeloma population; we did not observe a benefit among high-risk disease.
    Keywords:  autologous haematopoietic stem cell transplantation; maintenance; multiple myeloma; newly diagnosed multiple myeloma; selinexor
    DOI:  https://doi.org/10.1111/bjh.70851
  9. N Engl J Med. 2026 Sep 24. 395(12): 1233-1236
      
    DOI:  https://doi.org/10.1056/NEJMe2609181
  10. Genes (Basel). 2026 Sep 15. pii: 1122. [Epub ahead of print]17(9):
      Acute myeloid leukemia (AML) is cytogenetically and phenotypically heterogeneous, and this diversity contributes to differences in how patients respond to therapies that target apoptosis. Venetoclax, a selective BCL-2 inhibitor, has been demonstrated to improve outcomes when combined with hypomethylating drugs (HMAs) such as azacitidine or decitabine; nonetheless, clinical trials have indicated that resistance and recurrence are prevalent. This review examines the current evidence linking chromosomal abnormalities and cellular differentiation state to mitochondrial apoptotic pathways, with an emphasis on how these factors influence dependence on certain anti-apoptotic BCL-2 family proteins. We summarize how specific cytogenetic subtypes and high-risk groups (including monosomy 7/del(7q) and complex karyotype/TP53-altered AML) frequently show stress-adaptive signaling and reliance on multiple anti-apoptotic pathways, which can limit the durability of response to BCL-2 inhibition. Lineage-associated dependencies are also examined, such as monocytic differentiation (which leads to increased MCL-1 reliance) and erythroid/megakaryocytic differentiation, which has been associated with increased BCL-XL dependence and venetoclax resistance. Finally, we discuss the therapeutic implications of dependence mapping, including venetoclax combinations and direct MCL-1/BCL-XL targeting, and propose promising biomarker strategies that can detect dependence shifts early and guide appropriate treatment selection.
    Keywords:  BCL-2 family proteins; BH3 mimetics; acute myeloid leukemia; cytogenetics; mitochondrial apoptosis; targeted therapy; therapeutic resistance; venetoclax
    DOI:  https://doi.org/10.3390/genes17091122
  11. Clin Exp Immunol. 2026 Sep 26. pii: uxag059. [Epub ahead of print]
       INTRODUCTION: Selinexor is a first in class selective inhibitor of nuclear export (SINE) targeting Exportin-1 (XPO1) and approved for the treatment of multiple myeloma (MM). Selinexor has previously been shown to enhance natural killer (NK) cell activation against lymphoma cells via disruption of the NKG2A: HLA-E immune checkpoint axis.
    METHODS: MM cell lines (L363, U266, MM.1S) and primary myeloma cells isolated from the bone marrow of patients were exposed to selinexor (50-2000 nM) with or without IFNγ or IL-6 to mimic the tumour microenvironment (TME). Surface HLA-E and total HLA class I were quantified by flow cytometry. Immunoblotting and a range of functional assays were used to examine the effect of selinexor on NK cell effector function against MM.
    RESULTS: Selinexor downregulated surface HLA-E expression on MM cell lines and primary myeloma cells. This improved the activation of NKG2A+ NK cells, NK cell-specific lysis of MM cell lines and antibody-dependent cellular cytotoxicity (ADCC) with the therapeutic antibodies daratumumab and elotuzumab. This improvement was also observed in the presence of TME-mimicking signals IFNγ and IL-6. Pre-treatment of MM cells with selinexor for 24 hours prior to daratumumab resulted in optimal ADCC.
    DISCUSSION: These data reveal that selinexor selectively disrupts the NKG2A:HLA-E immune checkpoint axis in MM and enhances NK cell activation and ADCC against MM cells. These findings provide a mechanistic rationale for investigating combinations of selinexor with approved therapeutic antibodies in MM and suggest that treatment timing may be an important consideration in the design of combination regimens.
    Keywords:  HLA-E; Multiple myeloma; NK cells; NKG2A; XPO1; selinexor
    DOI:  https://doi.org/10.1093/cei/uxag059
  12. Medicine (Baltimore). 2026 Sep 25. 105(39): e50847
       RATIONALE: Central nervous system (CNS) involvement following blast crisis (BC) of chronic myeloid leukemia (CML) represents a challenging complication, particularly when atypical symptoms such as progressive vision loss obscure the diagnosis and delay timely intervention.
    PATIENT CONCERNS: A 65-year-old male presented with isolated CNS relapse following CML-BC, manifesting as progressive visual loss. Despite being in intramedullary complete remission and having received prophylactic intrathecal chemotherapy, the patient's atypical ocular symptom raised suspicion of CNS involvement.
    DIAGNOSES: Cerebrospinal fluid (CSF) analysis confirmed the presence of blast cells, establishing the diagnosis of CNS relapse.
    INTERVENTIONS: Treatment with intrathecal chemotherapy, systemic high-dose chemotherapy combined with tyrosine kinase inhibitor therapy.
    OUTCOMES: The patient demonstrated visual recovery and sustained disease remission at the 14-month follow-up.
    LESSONS: This case underscores the importance of clinical vigilance in patients with a history of leukemia who present with blurred vision or progressive vision impairment, as such manifestations,even in the absence of overt neurological symptoms, may be indicators of CNS relapse. Additionally, further investigation through animal models is warranted to characterize the blood-brain barrier penetrance of novel tyrosine kinase inhibitors (TKIs).
    Keywords:  Isolated central nervous system relapse; chronic myeloid leukemia; diagnostic and therapeutic considerations; tyrosine kinase inhibitors
    DOI:  https://doi.org/10.1097/MD.0000000000050847
  13. Free Radic Biol Med. 2026 Sep 21. pii: S0891-5849(26)01170-6. [Epub ahead of print]256 650-663
      Proteasome inhibitors, particularly bortezomib (BTZ) which induces oxidative stress, remain the cornerstone of multiple myeloma (MM) therapy. However, resistance driven by metabolic reprogramming and redox adaptation limits their long-term efficacy. Here, we identify a cholesterol biosynthesis-dependent antioxidant mechanism that shields MM cells from BTZ-induced generation of reactive oxygen species (ROS). High cholesterol biosynthesis activity characterizes BTZ-nonresponsive plasma cells and correlates with poor prognosis. Genetic silencing of SREBF2, the master transcriptional regulator of cholesterol metabolism, sensitized MM cells to BTZ both in vitro and in vivo. Pharmacological inhibition of HMG-CoA reductase, the rate-limiting enzyme of cholesterol biosynthesis, with the clinically approved atorvastatin likewise enhanced the anti-myeloma activity of BTZ in vitro and in vivo. Mechanistically, the lipid raft protein FLOT1 promoted FOXO3 nuclear translocation and SREBF2 activation, thereby driving increased cholesterol biosynthesis and accumulation of the intermediate metabolite 7-dehydrocholesterol (7-DHC), a critical antioxidant that mitigated BTZ-induced cytotoxicity. Decreasing 7-DHC production by disrupting SREBF2 activation or treating with atorvastatin impaired the cellular ROS detoxification capacity and enhanced BTZ-induced cytotoxicity. Collectively, our findings identify that MM cells resist therapy-induced ROS by accumulating 7-DHC through activation of cholesterol biosynthesis, and provide preclinical evidence for repurposing statins to augment the efficacy of BTZ therapy.
    Keywords:  7-Dehydrocholesterol; Bortezomib resistance; Cholesterol biosynthesis; Multiple myeloma; Oxidative stress
    DOI:  https://doi.org/10.1016/j.freeradbiomed.2026.09.019
  14. Leuk Res. 2026 Sep 16. pii: S0145-2126(26)00164-5. [Epub ahead of print]170 108320
       BACKGROUND: Classical Hodgkin lymphoma (cHL) is characterized by a prominent inflammatory microenvironment. However, the prognostic relevance of inflammation-based markers and their changes during treatment remains unclear. We evaluated baseline and interim inflammatory parameters in patients with cHL treated with ABVD.
    PATIENTS AND METHODS: This retrospective single-center study included 112 newly diagnosed patients with cHL treated with ABVD between 2012 and 2025. CAR, GPS, and mGPS were assessed at diagnosis and interim evaluation. Overall survival (OS) and progression-free survival (PFS) were analyzed using Kaplan-Meier and Cox regression methods.
    RESULTS: CRP, CAR, GPS, and mGPS decreased significantly during treatment (all p < 0.001), while higher baseline inflammatory scores were associated with advanced-stage disease (all p < 0.001). The 5-year PFS and OS rates were 77% and 95%, respectively. Baseline CAR, GPS, and mGPS were not independently associated with PFS. In the post-interim analysis, failure to achieve complete response (CR), higher CRP, and higher CAR were associated with poorer subsequent PFS. Interim CAR remained associated with PFS after adjustment for disease stage (HR 1.568, 95% CI 1.025-2.398; p = 0.038), but not after adjustment for interim response. Failure to achieve CR remained independently associated with poorer PFS after adjustment for stage and CAR (p = 0.012).
    CONCLUSION: Inflammation-based markers appear to reflect disease burden in cHL and improve during treatment. Although baseline markers showed limited prognostic value, higher interim CAR was associated with poorer subsequent PFS beyond disease stage, an association attenuated after accounting for treatment response. Dynamic assessment of systemic inflammation during treatment may therefore provide additional prognostic information in cHL.
    Keywords:  C reactive protein; Hodgkin lymphoma; Inflammation; Prognosis; Serum albumin
    DOI:  https://doi.org/10.1016/j.leukres.2026.108320
  15. Haematologica. 2026 Sep 24.
      Histologic transformation (HT) is the leading of death in follicular lymphoma (FL), yet outcomes remain poorly defined due to small cohorts and heterogenous definitions. To characterize outcomes and treatment patterns in the rituximab era we analyzed 344 patients with an initial biopsy-confirmed FL diagnosis between 2002 and 2022 who subsequently developed biopsy-confirmed HT in the Lymphoma Epidemiology of Outcomes (LEO) Consortium of Real-World Evidence (CReWE). Median age at HT was 64 (IQR 57-72). Initial treatment for HT (index therapy) included R-CHOP-like (n=154, 45%) and aggressive/salvage (n=85, 25%). The median event free survival (EFS) from HT was 9 months (95% CI, 7-11), and 2-year EFS was 30% (95% CI, 26%-36%). Median OS from HT was 4.9 years (95% CI, 4.0-7.5) with 2-year and 5-year OS estimates of 66% (95% CI, 61%-71%) and 49% (95% CI, 43%-56%), respectively. Relapses after HT occurred in 60%. Relapse histology included DLBCL 70%, FL 15%, and HGBCL 12%. Treatment following relapse from index therapy was commonly aggressive/salvage (often incorporating ASCT/CAR-T) in 44%. FLIPI (3-5), FL3A histology, IPI (4-5), ECOG >1, diagnosis to HT.
    DOI:  https://doi.org/10.3324/haematol.2026.300768
  16. Br J Haematol. 2026 Sep 20.
      Most patients treated for chronic lymphocytic leukaemia (CLL) fail to achieve measurable residual disease (MRD) negativity. The role of maintenance with the immunomodulatory drug lenalidomide in these patients is unclear. A randomised multicentre phase III trial (ACTRN12610000060044) was conducted in Australia and France to assess the effect of 2 years of daily lenalidomide maintenance versus observation in patients with CLL and residual disease after initial immunochemotherapy. The primary end-point was time to disease progression or death from randomisation. Between May 2011 and January 2018, 143 patients were randomised to receive lenalidomide (n = 71) or observation (n = 72). Median progression-free survival (PFS) was longer with lenalidomide at 64.6 months (95% confidence interval [CI] 47.7 to not reached) versus 42.4 months (95% CI 32.3-61.6) in the observation arm (p = 0.039). Lenalidomide benefit persisted for 3 years after maintenance cessation. There was no difference in overall survival. More patients taking lenalidomide achieved MRD negativity, especially those who received at least 20 maintenance cycles. Lenalidomide led to more cytopenias, infections and gastrointestinal effects. There were no cases of acute lymphoblastic leukaemia. In patients with CLL selected by the presence of residual disease at the end of initial chemoimmunotherapy, lenalidomide maintenance increased the chance of achieving MRD negativity and prolonged PFS.
    Keywords:  acute lymphoblastic leukaemia; chemoimmunotherapy; chronic lymphocytic leukaemia; flow cytometry; lenalidomide; maintenance; residual disease
    DOI:  https://doi.org/10.1111/bjh.70850